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先天性纤维肉瘤是一种罕见的软组织肿瘤，又称为婴儿型纤维肉瘤，主要见于新生儿和婴幼儿，好发于四肢远端如足、踝、手腕。本文报道1例胎儿期发现的腹膜后先天性纤维肉瘤，MRI上T1WI以稍低信号、T2WI以等信号为主，其内信号不均，增强后呈明显不均匀强化。病理免疫组化Pan-TRK(+),Vim(+),S100（部分+），Desmin（个别细胞+），CD34（局灶+），Ki-67（热点区约50%+）。出生后CT复查并穿刺活检，后大体病理结果证实为先天性/婴儿型纤维肉瘤。
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DOI：
中图分类号:R735.4
引用信息:
[1]彭芬,朱霞,张帅.胎儿腹膜后巨大先天性/婴儿型纤维肉瘤一例[J].影像诊断与介入放射学,2025,34(02):135-137.
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